The Middle-East connection of Wolman Disease

Authors

• Durjoy K. Shome, Department of Pathology, Salmaniya Medical Complex, PO Box 12, Manama, Bahrain. Fax. +973 279649. E-mail: shome{at}batelco.com.bh
• Emtethal Al-Jishi, Department of Pediatrics, Salmaniya Medical Complex, Manama, Bahrain.
• John F. Greally, Department of Pathology, Arabian Gulf University, College of Medicine and Medical Sciences, Manama, Bahrain.
• Neelam Malik, Department of Radiology, Salmaniya Medical Complex, Manama, Bahrain.
• Hassan A. Zainaldeen, Department of Pediatrics, Salmaniya Medical Complex, Manama, Bahrain.
• Nagalla S. Das, Department of Pathology, Salmaniya Medical Complex, Manama, Bahrain.

Abstract

The clinical, laboratory and cytological features of 2 Bahraini infants with Wolman9s disease are described. While one of the cases showed the classical diagnostic features, the other case exhibited a few atypical features such as lack of adrenal calcification and unusual morphology of vacuolated marrow macrophages. Literature review shows that this disorder may not be rare in this region.

Article Type

Case Report

First Page

597

Last Page

601

Recommended Citation

Shome, Durjoy K.; Al-Jishi, Emtethal; Greally, John F.; Malik, Neelam; Zainaldeen, Hassan A.; and Das, Nagalla S. (2002) "The Middle-East connection of Wolman Disease," Saudi Medical Journal: Vol. 23: Iss. 5, Article 25.
DOI: https://doi.org/10.15537/1658-3175.1715